Photic sneeze reflex in nephropathic cystinosis.

نویسندگان

  • B Katz
  • R B Melles
  • M R Swenson
  • J A Schneider
چکیده

Photic induced sneeze is a reflex that occurs in certain individuals after exposure to bright light. Cystinosis is an autosomal recessive inborn error of metabolism in which nonprotein cystine accumulates within lysosomes. The pathognomonic ocular manifestation of cystinosis is corneal crystal deposition. We observed photic induced sneezes during ophthalmoscopic examination in five of 19 patients with nephropathic cystinosis (26%). We report on this observation and discuss possible pathophysiological mechanisms for photic induced sneezing in cystinosis.

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عنوان ژورنال:
  • The British journal of ophthalmology

دوره 74 12  شماره 

صفحات  -

تاریخ انتشار 1990